Case list for Hereditary Hemorrhagic Telangiectasia (HHT), M. Osler
There is 1 CT case with this diagnosis.
Advanced stage, with bilomas
Hereditary telengiectasia. CT shows innumerable hypervascular foci representing arterio-venous malformations replacing a large volume of parenchyma, causing ischemia to liver parenchyma and bile ducts. Cystic spaces are biliary lakes (bilomas) due to ischemia. Note also multiple capsular vascular shunts, including shunts in the abdominal and thoracic wall. Diagnosis was confirmed upon hepatectomy following orthotopic liver transplantation.